Lumbo-Costo-Vertebral Syndrome: An Iceberg with Tip of Hernia and Body of Spinal and Neurological Malformations

We read with great interest the contribution of Gupta et al on the lumbo-costo-vertebral syndrome (LCVS).[1] We encountered this rare anomaly in a 39 week-of-gestation female patient, who after an uncomplicated birth underwent investigation because of a left lumbar hernia, and vertebral anomalies. Imaging assay with plain radiography, revealed the presence of tenth and eleventh thoracic hemivertebrae, and intervertebral cleft of the twelfth thoracic vertebra. These anomalies resulted in clockwise thoracic and counterclockwise lumbar scoliosis. Magnetic resonance imaging revealed syringomyelia at the level of the three lower thoracic dysplastic vertebrae, and low termination of the spinal cord at the level of the fourth lumbar vertebra.